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Chronic fatigue syndrome in young people: the spectrum and the myths
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British Journal of Hospital Medicine, September 2006, Vol 67, No 9
L
arge telephone surveys in both the
UK and USA suggest that chronic
fatigue syndrome/myalgic encepha-
lopathy (CFS/ME) in children is both
surprisingly common (0.19–2%), and
indiscriminate in who it affects (Jordan et
al, 2000; Chalder et al, 2003; Jones et al,
2004). There is no gender preference, no
social class gradient, and all ethnic groups
are affected. The CFS/ME described in
studies where patients are recruited from
specialist care is much rarer and predomi-
nantly affects white females of higher
socioeconomic status (Patel et al, 2003).
Why is there such a difference between
those seen in specialist care and those
described in the population? One explana-
tion is successful health-seeking behaviour
– families from a higher socioeconomic
class have a better chance of finding treat-
ment, especially when treatment is limited
or rationed.
Although this may explain the difference
in socioeconomic group, it doesn’t explain
the difference in gender ratio. Why are girls
much more likely to be seen in a specialist
clinic than boys? A population study from
Wichita suggests that girls are more likely to
present with recurrent sore throats and lym-
phadenopathy whereas boys are more likely
to complain of concentration and memory
problems (Jones et al, 2004). This may
mean that girls are more likely to present to
health services whereas boys are more likely
to present to education welfare officers
because of time missed from school.
These problems may be compounded by
the fact that many clinicians either do not
believe that CFS/ME is a real problem or
do not know how to treat it (Thomas and
Smith, 2005). Many feel unable to help and
are uncertain about treatment approaches.
There are several myths surrounding CFS/
ME that may promote this behaviour.
Debunking the myths
Myth 1: CFS/ME is just
yuppy ‘flu
This myth was generated in the 1980s
when the press latched onto descriptions
of this condition in those of higher social
economic class. This was probably a result
of successful health-seeking behaviour. As
CFS/ME affects every social class and eth-
nic groups equally, the real issue is actually
about those who are unable to access treat-
ment and support.
Myth 2: CFS/ME is only seen in
high achievers
The only longitudinal study looking at
this question (Viner and Hotopf, 2004)
showed that academic ability was not asso-
ciated with the risk of lifetime self-report-
ed CFS/ME. This is consistent with popu-
lation studies which do not show a social
class gradient although it is possible that
high achievers and their families are more
likely to present to specialist services.
Myth 3: CFS/ME is psychological
Between 25 and 70% of young people
have an associated psychiatric disorder
such as depression, somatization or anxiety
(Carter et al, 1999; Garralda et al, 1999;
van Middendorp et al, 2001; Chalder et al,
2003). Adolescents with CFS/ME have
also been reported as having more psycho-
logical distress then young people with
either juvenile rheumatoid arthritis or
cystic fibrosis. However, none of these
studies have been able to demonstrate the
direction of causality. The high level of
anxiety and low mood seen could be a
result of suffering from a severe chronic
disabling condition. The presence of anxi-
ety and low mood may also increase refer-
ral to a specialist centre thereby increasing
the prevalence in these cohorts.
The only longitudinal study to investi-
gate this (Viner and Hotopf, 2004) demon-
strated convincingly that maternal psycho-
pathology, parental illness, childhood or
adolescent psychological distress, academic
ability, atopy, birth order, birth weight and
obesity are not associated with the risk of
lifetime self-reported or physician-diag-
nosed CFS/ME. As with other conditions,
it is possible that the presence of anxiety
and low mood may worsen prognosis or
make it harder to access rehabilitation. It is
therefore important to identify these co-
morbid conditions but unhelpful to ascribe
them as the cause of the condition.
Myth 4: Young people with CFS/
ME never get better
Current evidence suggests that the prog-
nosis for children (under 16 years) is good
with at least 84% making a good or full
recovery (Joyce et al, 1997). This is in
contrast with the prognosis in adults which
is much worse.
How does CFS/ME present in
children and young people?
The Royal College of Paediatrics and
Child Health (RCPCH) (2004) defines
CFS/ME in young people as disabling
fatigue without another cause (Table 1). In
the RCPCH definition there is no mini-
mum time requirement for the fatigue and
Chronic fatigue syndrome in young
people: the spectrum and the myths
RCPCH definition Generalized fatigue persisting after routine tests and investigations have failed to
for CFS/ME
identify an obvious underlying ‘cause’. In CFS/ME the fatigue is likely to be associated with
other classical symptoms and is classically exacerbated by effort (both mental and physical)
Other classical Severe malaise, headaches, sleep disturbances, concentration difficulties, memory
symptoms
impairment, depressed mood, myalgia/muscle pain at rest and on exercise, nausea,
sore throat, tender lymph nodes, abdominal pain and arthralgia/joint pain
Symptoms
Feeling too hot or cold, dizziness, cough, eye pain/increased sensitivity to light
reported less
(photophobia), vision or hearing disturbances (hyperacusis), weight loss or gain,
often
muscle weakness, lack of energy for usual activities and diarrhoea
From RCPCH (2004)
Table 1. Royal College of Paediatrics and Child Health (RCPCH) definition for
chronic fatigue syndrome/myalgic encephalitis (CFS/ME)

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no required symptoms, although common
and less common symptoms are described.
This is in contrast with the Centers for
Disease Control and Prevention (CDC)
definition for adults which requires
6 months of fatigue and at least four other
symptoms (Fukuda et al, 1994).
The fatigue in CFS/ME must be disa-
bling, i.e. severe enough to result in a
reduction of activities. The fatigue and
other symptoms are made worse (payback)
by exertion whether the exertion is physi-
cal, emotional or cognitive. The payback is
often delayed to the following day or later,
and can last a day or longer. When children
are moderately to severely affected, they
can get payback after what appears to be a
very small increase in activity. This may
present as children doing alternate days at
school or having increased symptoms after,
for example, home tuition. It is important
to recognize this when planning rehabilita-
tion programmes otherwise the rehabilita-
tion itself can make the illness worse.
In addition to the fatigue, an almost
universal complaint is sleep disturbance.
Usually children and adults find it hard to
get off to sleep or describe a restless or
broken sleep. They usually find it very dif-
ficult to get up in the morning and do not
feel refreshed after they sleep. Unrefreshing
sleep is part of the CDC criteria for CFS/
ME in adults and is a useful clinical sign.
There are many other symptoms
described in CFS/ME both in definitions
and in population studies. It is important
to recognize that not all children will talk
about fatigue at presentation. Children
may present with concentration and mem-
ory problems which is consistent with
population studies which have shown this
is a significant problem. The memory
problems appear to be short- and medium-
term problems which are very disruptive
for children attending school. Young peo-
ple talk about having a lesson one day and
forgetting the content the next day. This is
in addition to the concentration problems
as they phase in and out of conversations,
making learning even more difficult.
Recurrent sore throats and lymphadeno-
pathy, headaches, muscle and joint pain
are part of the adult CDC definition for
CFS/ME and these symptoms are com-
monly seen in children. Children may get
labelled as having recurrent ‘tonsillitis’
every 2–3 weeks because they keep pre-
senting with sore throat, tender lymph
nodes, muscle and joint pain. The diagno-
sis of CFS/ME must be considered for a
child who presents in this way if there is
associated disabling fatigue.
The severity and therefore presentation
of this condition is very variable. Some
children are only mildly affected and able
to attend full-time school but do nothing
when they go home, or miss school regu-
larly at the end of the week. At the other
end of the spectrum, some children and
young people are so severely affected that
they are unable to get out of bed. Their
symptoms are similar to those described
above but much more severe. They are
likely to have noise and light sensitivity
and may be sensitive to smells (such as
perfumes), medication and some food
types. Very little is known about this
group of patients and almost nothing is
published, but clinical experience is that
most do well with the right support, help
and rehabilitation programme.
If one sees a child or young person with
CFS/ME it is important to exclude other
medical or psychological causes for the
fatigue. Screening investigations are impor-
tant and history and examination may
point to other investigations which are
necessary. Blood screening investigations
should include full blood count, erythro-
cyte sedimentation rate or viscosity; C-
reactive protein; urea, electrolytes and
creatinine; liver function tests, random
glucose, thyroid function, CPK, ferritin
and coeliac screen. The urine should be
dipped for protein, blood and glucose.
Conclusions
CFS/ME is common and affects children
and young people from every background.
Clinicians are poor at both recognizing the
condition and treating it. With correct
management and support, however, the
outlook for children and young people
with this condition is much better than
many clinicians realize.
BJHM
Esther Crawley
Consultant Paediatrician and Clinical Lead
Bath/Bristol Paediatric CFS/ME Service
Royal United Hospital
Bath BA1 3NG
Carter BD, Kronenberger WG, Edwards JF,
Marshall GS, Schikler KN, Causey DL (1999)
Psychological symptoms in chronic fatigue and
juvenile rheumatoid arthritis. Pediatrics 103(5 pt
1): 975–9
Chalder T, Goodman R, Wessely S, Hotopf M,
Meltzer H (2003) Epidemiology of chronic
fatigue syndrome and self reported myalgic
encephalomyelitis in 5-15 year olds: cross
sectional study. BMJ 327(7416): 654–5
Fukuda K, Straus SE, Hickie I, Sharpe MC,
Dobbins JG, Komaroff A (1994) The chronic
fatigue syndrome: a comprehensive approach to
its definition and study. International Chronic
Fatigue Syndrome Study Group. Ann Intern Med
121(12): 953–9
Garralda E, Rangel L, Levin M, Roberts H,
Ukoumunne O (1999) Psychiatric adjustment in
adolescents with a history of chronic fatigue
syndrome. J Am Acad Child Adolesc Psychiatry
38(12): 1515–21
Jones JF, Nisenbaum R, Solomon L, Reyes M,
Reeves WC (2004) Chronic fatigue syndrome
and other fatiguing illnesses in adolescents: a
population-based study. J Adolesc Health 35(1):
34–40
Jordan KM, Ayers PM, Jahn SC, Taylor KK,
Huuang C, Richman J, Jason LA (2000)
Prevalence of fatigue and chronic fatigue
syndrome-like illness in children and adolescents.
J Chronic Fatigue Syndr 6: 3–21
Joyce J, Hotopf M, Wessely S (1997) The prognosis
of chronic fatigue and chronic fatigue syndrome:
a systematic review. QJM 90(3): 223–33
Patel MX, Smith DG, Chalder T, Wessely S (2003)
Chronic fatigue syndrome in children: a cross
sectional survey. Arch Dis Child 88(10): 894–8
Royal College of Paediatrics and Child Health
(2004) Evidence Based Guideline for the
Management of CFS/ME (Chronic Fatigue
Syndrome/myalgic Encephalopathy) in Children and
Young People. Royal College of Paediatrics and
Child Health, London
Thomas MA, Smith AP (2005) Primary healthcare
provision and chronic fatigue syndrome: a survey
of patients’ and General Practitioners’ beliefs.
BMC Fam Pract 6: 49
van Middendorp H, Geenen R, Kuis W, Heijnen
CJ, Sinnema G (2001) Psychological adjustment
of adolescent girls with chronic fatigue syndrome.
Pediatrics 107(3): E35
Viner R, Hotopf M (2004) Childhood predictors of
self reported chronic fatigue syndrome/myalgic
encephalomyelitis in adults: national birth cohort
study. BMJ 329(7472): 941
Further reading
Department of Health (2004) Chronic fatigue
syndrome (CFS) and myalgic encephalopathy (ME)
exemplar. Department of Health/Department for
Education and Skills, London
kEY pointS
n Chronic fatigue syndrome/myalgic
encephalitis (CFS/ME) is surprisingly
common in children.
n CFS/ME may present as recurrent
tonsillitis or with memory and
concentration problems.
n The prognosis in children is good and it
is therefore important to offer effective
rehabilitation.